Adenocarcinoma da ampola de vater associado com neurofibromatose de von recklinghausen

Translated title of the contribution: Adenocarcinoma of Vater's Ampulla associated with Von Recklinghausen's Neurofibromatosis

Helena Gomes, Rui Lebre, Jorge Fonseca, Paula Borralho, Reis Duarte

Research output: Contribution to journalArticlepeer-review

3 Citations (Scopus)

Abstract

Von Recklinghausen's Neurofibromatosis is an autosomal dominant disease of variable manifestations. Association with gastrointestinal and hepatobiliary tumours is well documented, most of them being benign neurofibromas. Other tumours, such as leiomyomas, sarcomas, ganglioneuromas and carcinoids are less frequent. Much rarer is the development of epithelial malignancies and an ontogenic relation is not clear. The authors report a case of adenocarcinoma of Vater's Ampulla and duodenal neurofibromas, in a patient with Von Recklinghausen's disease, presenting obstuctive jaundice.

Translated title of the contributionAdenocarcinoma of Vater's Ampulla associated with Von Recklinghausen's Neurofibromatosis
Original languagePortuguese (Brazil)
Pages (from-to)833-836
Number of pages4
JournalActa Medica Portuguesa
Volume10
Issue number11
Publication statusPublished - 1997
Externally publishedYes

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